Revista de Odontologia da UNESP
https://revodontolunesp.com.br/article/588018d07f8c9d0a098b4e2a
Revista de Odontologia da UNESP
Original Article

Cleidocranial dysostosis - case report of a multidisciplinary approach

Disostose cleidocraniana - relato de um caso clínico com abordagem multidisciplinar

Urzal, Vanda; Pinhão Ferreira, Afonso; Figueiredo, Adriano

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Abstract

Cleidocranial dysostosis (CCD) is a rare genetic syndrome, autosomal dominant. In this paper a patient with cleidocranial dysostosis was treated under a multidisciplinary basis. Many treatment challenges were solved by a dental team, in which the orthodontic traction of unerupted teeth associated with bimaxilar surgery had the main focus. The aim of this surgical-orthodontic treatment was to restore the functional occlusion and to improve the facial aesthetics, taking advantage of all the impacted teeth which characterize this syndrome.

Keywords

Cleidocranial dysostosis, orthodontic treatment, orthognatic surgery

Resumo

A disostose cleidocraniana é uma síndrome genética rara, autossómica dominante. Neste caso particular, os muitos desafios dos tratamentos foram resolvidos por uma equipe odontológica, cujo traccionamento ortodôntico de dentes inclusos associados com a cirurgia ortognática bimaxilar foi o principal foco. O objectivo deste tratamento ortodôntico-cirúrgico foi restaurar a oclusão funcional e melhorar a estética facial, aproveitando a vantagem de todos os dentes impactados que caracterizam esta síndrome.

Palavras-chave

Disostose cleidocraniana, tratamento ortodôntico, cirurgia ortognática

References



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