Cleidocranial dysostosis - case report of a multidisciplinary approach
Disostose cleidocraniana - relato de um caso clínico com abordagem multidisciplinar
Urzal, Vanda; Pinhão Ferreira, Afonso; Figueiredo, Adriano
Rev. odontol. UNESP, vol.40, n1, p.53-57, 2011
Abstract
Cleidocranial dysostosis (CCD) is a rare genetic syndrome, autosomal dominant. In this paper a patient with cleidocranial dysostosis was treated under a multidisciplinary basis. Many treatment challenges were solved by a dental team, in which the orthodontic traction of unerupted teeth associated with bimaxilar surgery had the main focus. The aim of this surgical-orthodontic treatment was to restore the functional occlusion and to improve the facial aesthetics, taking advantage of all the impacted teeth which characterize this syndrome.
Keywords
Cleidocranial dysostosis, orthodontic treatment, orthognatic surgery
Resumo
A disostose cleidocraniana é uma síndrome genética rara, autossómica dominante. Neste caso particular, os muitos desafios dos tratamentos foram resolvidos por uma equipe odontológica, cujo traccionamento ortodôntico de dentes inclusos associados com a cirurgia ortognática bimaxilar foi o principal foco. O objectivo deste tratamento ortodôntico-cirúrgico foi restaurar a oclusão funcional e melhorar a estética facial, aproveitando a vantagem de todos os dentes impactados que caracterizam esta síndrome.
Palavras-chave
Disostose cleidocraniana, tratamento ortodôntico, cirurgia ortognática
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