Revista de Odontologia da UNESP
https://revodontolunesp.com.br/article/588018d07f8c9d0a098b4e2a
Revista de Odontologia da UNESP
Original Article

Cleidocranial dysostosis - case report of a multidisciplinary approach

Disostose cleidocraniana - relato de um caso clínico com abordagem multidisciplinar

Urzal, Vanda; Pinhão Ferreira, Afonso; Figueiredo, Adriano

Downloads: 0
Views: 398

Abstract

Cleidocranial dysostosis (CCD) is a rare genetic syndrome, autosomal dominant. In this paper a patient with cleidocranial dysostosis was treated under a multidisciplinary basis. Many treatment challenges were solved by a dental team, in which the orthodontic traction of unerupted teeth associated with bimaxilar surgery had the main focus. The aim of this surgical-orthodontic treatment was to restore the functional occlusion and to improve the facial aesthetics, taking advantage of all the impacted teeth which characterize this syndrome.

Keywords

Cleidocranial dysostosis, orthodontic treatment, orthognatic surgery

Resumo

A disostose cleidocraniana é uma síndrome genética rara, autossómica dominante. Neste caso particular, os muitos desafios dos tratamentos foram resolvidos por uma equipe odontológica, cujo traccionamento ortodôntico de dentes inclusos associados com a cirurgia ortognática bimaxilar foi o principal foco. O objectivo deste tratamento ortodôntico-cirúrgico foi restaurar a oclusão funcional e melhorar a estética facial, aproveitando a vantagem de todos os dentes impactados que caracterizam esta síndrome.

Palavras-chave

Disostose cleidocraniana, tratamento ortodôntico, cirurgia ortognática

References



1. Currall V, Clancy R, Dimond D, Amirfeyz R, Kershaw C, Gargan M. Cleidocranial dysplasia. Current Orthopaedics 2007; 21: 159-62.

2. Hemalatha R, Balasubramaniam MR. Cleidocranial dysplasia: a case report. J Indian Soc Pedod Prev Dent. 2008; 26: 40-3.

3. Suda N, Hamada T, Hattori M, Torii C, Kosaki K, Moriyama K. Diversity of supernumerary tooth formation in siblings with cleidocranial dysplasia having identical mutation in RUNX2 : possible involvement of non-genetic or epigenetic regulation.Orthod Craniofac Res. 2007; 10: 222-5.

4. McGuire TP, Gomes PP, Lam DK, Sandor GKB. Cranioplasty for midline metopic suture defects in adults with cleidocranial dysplasia. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2007; 103: 175-9.

5. Farronato G, Maspero C, Farronato D, Gioventù S. Orthodontic treatment in a patient with cleidocranial dysostosis. Angle Orthodont. 2009; 79: 178-85.

6. Angle AD, Rebellato J. Dental team management for a patient with cleidocranial dysostosis. Am J Orthod Dentofacial Orthop. 2005; 128: 110-7.

7. Becker A, Lustmann J, Shteyer A. Cleidocranial dysplasia: part 1- general principles of the orthodontic and surgical treatment modality. Am J Orthod Dentofacial Orthop. 1997; 111: 28-33.

8. Bathi RJ, Masur VN. Pyknodysostosis - a report of two cases with a brief review of the literature. Int J Oral Maxillofac Surg. 2000; 29: 439‑42.

9. Richardson A, Deussen FF. Facial and dental anomalies in cleidocranial dysplasia: a study of 17 cases. Int J Paediatr Dent. 1994; 4: 225-31.

10. Bayar GR, Ortako K, Sencimen M. Multiple impacted teeth: report of 3 cases. Eur J Dent. 2008; 1: 73-8.
588018d07f8c9d0a098b4e2a rou Articles
Links & Downloads

Rev. odontol. UNESP

Share this page
Page Sections